Hypoplastic Left Heart Syndrome (HLHS)

Hypoplastic Left Heart Syndrome (HLHS)

Hypoplastic Left Heart Syndrome (HLHS). The term “hypoplastic” refers to underdevelopment
of a tissue or organ. In HLHS, most of the left-sided heart structures
are hypoplastic. This is a view from inside the right atrium. An atrial septal defect, or ASD, is a hole
between the right and left atria. This is a view from inside the left atrium. The mitral valve is also hypoplastic and is
either severely narrowed or not formed at all. The abnormal mitral valve prevents blood from
entering the left ventricle. Blood flow is then diverted across the ASD and into the
right atrium. Blood return from both the lungs and body flows into the right ventricle. The
right ventricle pumps blood to both the lungs and the body. This is why HLHS is referred
to as a “single ventricle” defect. In HLHS, a PDA (Patent Ductus Arteriosus)
exists to provide blood flow from the pulmonary artery to the body. Babies with HLHS have
a bluish appearance, known as cyanosis, as a result of mixing oxygen-rich and oxygen-poor
blood. If the PDA closes, the baby will become critically ill. A continuous IV medication
called prostaglandin is needed to keep the PDA open after birth. Surgery is typically performed within the
first few weeks of life.

9 Replies to “Hypoplastic Left Heart Syndrome (HLHS)”

  1. Hello! My name is Stephanie, I'm 29 years old and I have HLHS, TGA, ASD, VSD and severe MVS and had all of my surgeries at Cincinnati Childrens!!! I was one of the first people to have the Fontan there, Thank you Cinci Childrens for saving my Life. <3 Love to Dr. Bailey, my surgeon!!!!! <3 Here is my page with a blog and all of my YouTube videos if you'd ever like to get in touch contact me anytime, thank you and God Bless <3  halfaheartvstheworld.blogspot.com/

  2. very informative video .I am in Pakistan ..my baby is born with HLHS .,in Pakistan we have no any facility to treat this disease ..
    AS a father it,s so difficult to see your children in difficulties …pray for my baby ..

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